Foix-Alajouanine syndrome mimicking a spinal cord tumor.

نویسندگان

  • Renan Salomão
  • Nathalie Henriques Silva Canêdo
  • Guilherme P Abrão
  • Carlos Lima
  • Marcus André Acioly
چکیده

Subacute necrotizing myelopathy (SNM) or Foix-Alajouanine syndrome is a rare disease characterized by progressive neurological dysfunction caused by a spinal dural arteriovenous fistula (AVF). Radiological diagnosis is usually suspected when there is intramedullary nonspecific enhancement and perimedullary flow voids. Ring-enhancement is rarely reported in the scope of AVF, which poses a diagnostic challenge and raises the suspicion of a spinal cord tumor. In such situations, biopsy can be required and delay proper diagnosis. We report the case of a patient with SNM, who underwent biopsy on the assumption of it being a spinal cord tumor.

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Congestive Myelopathy due to Intradural Spinal AVM Supplied by Artery of Adamkiewicz: Case Report with Brief Literature Review and Analysis of the Foix-Alajouanine Syndrome Definition

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عنوان ژورنال:
  • Revista da Associacao Medica Brasileira

دوره 63 7  شماره 

صفحات  -

تاریخ انتشار 2017